Management of Two Years Old Child with Russell-Silver Syndrome - A Case Report

نویسندگان

چکیده

Russell-Silver syndrome (RSS) is a rare genetic malformation characterized by the growth of 2-year-old male child with RSS who underwent hip spica surgery under general anesthesia. The patient had history mild developmental delay, failure to gain weight, and frequent vomiting. Anesthetic implications RSS, including airway management, glucose homeostasis, hypothermia, pharmacological considerations, were considered during patient's pre-operative assessment intraoperative management. was induced propofol fentanyl, maintenance anesthesia achieved sevoflurane. safely secured, extubation performed smoothly. anesthetic management proceeded without complications, ensuring successful outcome. This case report highlights importance considering specific in perioperative patients this syndrome.

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ژورنال

عنوان ژورنال: Journal of the Bahrain Medical Society

سال: 2023

ISSN: ['1015-6321', '2536-0019']

DOI: https://doi.org/10.26715/jbms.35_2_5